ChemicalBook > CAS DataBase List > 3-butanoyloxy-4-trimethylammonio-butanoate

3-butanoyloxy-4-trimethylammonio-butanoate

Product Name
3-butanoyloxy-4-trimethylammonio-butanoate
CAS No.
25576-40-3
Chemical Name
3-butanoyloxy-4-trimethylammonio-butanoate
Synonyms
Butyrylcarnitine;Butyrylcarnitine29;Butyryl-L-carnitine;R-Butyryl Carnitine;O-butanoyl-L-carnitine;n-Butyryl-L(-)-carnitine;L-Carnitine butyryl ester;Butyryl-L-carnitine;Butyryl-L-carnitine >=97.0% (TLC);3-butanoyloxy-4-trimethylammonio-butanoate
CBNumber
CB71235723
Molecular Formula
C11H21NO4
Formula Weight
231.29
MOL File
25576-40-3.mol
More
Less

3-butanoyloxy-4-trimethylammonio-butanoate Property

storage temp. 
2-8°C
solubility 
soluble in Methanol, Water
form 
Solid
color 
White
optical activity
[α]/D -23±2°, c = 1 in H2O
More
Less

Hazard and Precautionary Statements (GHS)

More
Less

N-Bromosuccinimide Price

Sigma-Aldrich
Product number
42623
Product name
Butyryl-L-carnitine
Purity
≥97.0% (TLC)
Packaging
10MG
Price
$101
Updated
2025/07/31
Sigma-Aldrich
Product number
42623
Product name
Butyryl-L-carnitine
Purity
≥97.0% (TLC)
Packaging
50MG
Price
$398
Updated
2025/07/31
Sigma-Aldrich
Product number
08984
Product name
Butyryl-L-carnitine
Purity
analytical standard
Packaging
10MG
Price
$129
Updated
2025/07/31
ChemScene
Product number
CS-0062329
Product name
Butyrylcarnitine
Purity
>99.0%
Packaging
1mg
Price
$55
Updated
2021/12/16
ChemScene
Product number
CS-0062329
Product name
Butyrylcarnitine
Purity
>99.0%
Packaging
5mg
Price
$150
Updated
2021/12/16
More
Less

3-butanoyloxy-4-trimethylammonio-butanoate Chemical Properties,Usage,Production

Uses

A potential prodrug, via the carnitine transporter OCTN2 and the amino acid transporter ATB0,+

Uses

Butyryl-L-carnitine may be used as an analytical reference standard for the separation and identification of underivatized butyryl-L-carnitine in human plasma samples using high-performance liquid chromatography coupled to tandem mass spectrometry (HPLC-MS/MS). It may also be used as an analytical reference standard for the quantification of the analyte in biological samples using chromatography-based techniques.

Definition

ChEBI: An optically active form of O-butanoylcarnitine having L-configuration.

General Description

Butyryl-L-carnitine is a naturally occurring compound belonging to the acylcarnitine class of compounds as listed in the human metabolome database (HMBD). These compounds are reported to be used as biomarkers in the diagnosis of carnitine deficiency. It acts as a carrier of long chain acyl groups from activated fatty acids across the inner mitochondrial membrane into the mitochondrial matrix where they undergo β-oxidation to acetyl CoA to obtain usable energy via the citric acid cycle.

Biochem/physiol Actions

Butyrylcarnitine is elevated in patients with Acyl-CoA dehydrogenase, short-chain (SCAD) deficiency, in infants with acute acidosis and generalized muscle weakness and in middle-aged patients with chronic myopathy localized in muscle; very long chain Acyl-CoA dehydrogenase deficiency, and celiac disease.

3-butanoyloxy-4-trimethylammonio-butanoate Preparation Products And Raw materials

Raw materials

Preparation Products

More
Less

3-butanoyloxy-4-trimethylammonio-butanoate Suppliers

Toronto Research Chemicals
Tel
--
Fax
--
Email
info@trc-canada.com
Country
Canada
ProdList
6038
Advantage
71

25576-40-3, 3-butanoyloxy-4-trimethylammonio-butanoateRelated Search:


  • 3-butanoyloxy-4-trimethylammonio-butanoate
  • Butyrylcarnitine
  • (3R)-3-butanoyloxy-4-trimethylammonio-butanoate
  • (2R)-3-Carboxy-N,N,N-trimethyl-2-(1-oxobutoxy)-1-propanaminium Inner Salt
  • Butyryl-L-carnitine
  • L-Carnitine butyryl ester
  • n-Butyryl-L(-)-carnitine
  • R-Butyryl Carnitine
  • O-butanoyl-L-carnitine
  • Butyryl-L-carnitine >=97.0% (TLC)
  • Butyrylcarnitine29
  • Butyryl-<sc>L</sc>-carnitine
  • 25576-40-3
  • Amino Acids 13C, 2H, 15N
  • Amino Acids & Derivatives
  • Chiral Reagents
  • Intermediates & Fine Chemicals
  • Pharmaceuticals