N-ISOVALERYLGLYCINE Chemical Properties

Melting point:

105°C

Boiling point:

371.8±25.0 °C(Predicted)

Density 

1.097±0.06 g/cm3(Predicted)

storage temp. 

Sealed in dry,Room Temperature

solubility 

DMSO (Slightly), Methanol (Slightly)

pka

3.58±0.10(Predicted)

form 

Solid

color 

White to Off-White

BRN 

1766622

Safety Information

Hazard Codes 

Xi

Risk Statements 

36

Safety Statements 

22-24/25

HazardClass 

IRRITANT

HS Code 

2924297099

N-ISOVALERYLGLYCINE Usage And Synthesis

Description

Isovaleroylglycine is a compound found in the urine of patients with isovaleric acidemia, a disorder created by defective leucine metabolism due to a deficiency in the isovaleryl coenzyme A dehydrogenase. It has been used as a diagnostic tool in the diagnosis of various acidemias and mitochondrial fatty acid β-oxidation defects.

Chemical Properties

White to Off-White Solid

Uses

N-Isovalerylglycine is a useful diagnostic tool in the diagnosis of many organic acidemias and mitochondrial fatty acid β-oxidation defects. N-Isovalerylglycine is found in the urine of patients with isovaleric acidemia, an inborn error of leucine metabolism.

Definition

ChEBI: An N-acylglycine in which the acyl group is specified as isovaleryl.

N-ISOVALERYLGLYCINE(16284-60-9)Related Product Information

• Z-VAL-PHE-OH
• N-CBZ-VAL-TYR METHYL ESTER
• H-VAL-ALA-OH
• VALINOMYCIN
• H-ILE-ALA-OH
• H-VAL-TYR-OH
• H-VAL-ASP-OH
• Z-VAL-ILE-OH
• H-VAL-GLY-OH
• H-VAL-PHE-OH
• Z-VAL-ALA-OH
• Z-ILE-PHE-OH
• H-ILE-PHE-OH
• Z-VAL-MET-OH
• Z-ILE-GLY-OH
• H-VAL-VAL-OH
• Z-ILE-ILE-OH
• N-Isovalerylglycine-2,2-D2