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Glutaroyl carnitine

Product Name
Glutaroyl carnitine
CAS No.
102636-82-8
Chemical Name
Glutaroyl carnitine
Synonyms
Glutaroyl carnitine;Glutaryl L-Carnitine;DL-Glutaryl Carnitine;(L)-Glutaryl Carnitine;O-glutaroyl-L-carnitine;Glutarylcarnitine in Water;Glutarylcarnitine lithium salt;Glutaroyl N-(methyl-D3)-carnitine;Glutamyl-L-carnitine lithium salt;Glutaryl-L-carnitine lithium salt
CBNumber
CB31565246
Molecular Formula
C12H21NO6
Formula Weight
0
MOL File
102636-82-8.mol
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Glutaroyl carnitine Property

storage temp. 
2-8°C
solubility 
DMSO, Methanol, Water
form 
Gel
color 
Clear Colourless
Appearance
white solid
optical activity
[α]/D -20±2°, c = 1 in H2O
Stability:
Very Hygroscopic
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Hazard and Precautionary Statements (GHS)

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N-Bromosuccinimide Price

Sigma-Aldrich
Product number
72715
Product name
Glutaryl-L-carnitine lithium salt
Purity
≥98.0% (TLC)
Packaging
10MG
Price
$101
Updated
2025/07/31
Sigma-Aldrich
Product number
72715
Product name
Glutaryl-L-carnitine lithium salt
Purity
≥98.0% (TLC)
Packaging
50MG
Price
$382
Updated
2025/07/31
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Glutaroyl carnitine Chemical Properties,Usage,Production

Description

The role of glutarylcarnitine in the body, like that of other acylcarnitines, is in facilitating the transport of fatty acids into mitochondria for beta-oxidation, therefore glutarylcarnitine is used in the diagnosis of metabolic disorders.


The product is used primarily as a control for MS/MS.


Glutarylcarnitine has a wide range of potential uses in both research and clinical applications. Glutarylcarnitine and carnosylcarnitine may be biomarkers for the diagnosis of autism spectrum disorders. Glutarylcarnitine has been studied as a potential therapeutic agent in the treatment of diabetes, metabolic syndrome, and obesity.

Chemical Properties

Clear Thick Gel

Uses

A metabolite of L-Carnitine (C184110).

Definition

ChEBI: O-glutaroyl-L-carnitine is an O-acyl-L-carnitine in which the acyl group is specified as glutaroyl. It has a role as a human metabolite. It is functionally related to a glutaric acid.

Biochem/physiol Actions

Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction.

IC 50

Human Endogenous Metabolite

Glutaroyl carnitine Preparation Products And Raw materials

Raw materials

Preparation Products

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Glutaroyl carnitine Suppliers

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102636-82-8, Glutaroyl carnitineRelated Search:


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