β-Hydroxyisovaleric Acid-d8 Chemical Properties

solubility 

Chloroform (Slightly), DMSO (Sparingly), Methanol (Slightly)

form 

Oil

color 

Colourless to Yellow

β-Hydroxyisovaleric Acid-d8 Usage And Synthesis

Uses

b-Hydroxyisovaleric Acid-d8 is the isotope labelled analog of b-Hydroxyisovaleric Acid (H943605); a metabolite of the essential amino acid Leucine. It is synthesized in the human body and studies suggest that b-Hydroxyisovaleric Acid may have an effect on increasing muscle weight and strength. The presence of elevated b-Hydroxyisovaleric Acid is a sensitive marker of biotin deficiency and may indicate the presence of a genetic disorder such as biotinidase deficiency or holocarboxylase synthetase deficiency.

Definition

ChEBI: 3-hydroxyisovaleric acid is a 3-hydroxy monocarboxylic acid that is isovaleric acid substituted at position 3 by a hydroxy group. Used as indicator of biotin deficiency. It has a role as a human metabolite. It is functionally related to a butyric acid and an isovaleric acid. It is a conjugate acid of a 3-hydroxyisovalerate.

β-Hydroxyisovaleric Acid-d8(123743-99-7)Related Product Information

• beta-Hydroxyisovaleric Acid